A case of pachydermodactyly in a 16 year-old male
نویسندگان
چکیده
Background Pachydermodactyly is a rare benign superficial fibromatosis, aetiology unknown, characterized by asymmetric painless swelling of the proximal interphalangeal (PIF) joints of the hands, most frequently in adolescent males. Radiographs and MRI show only soft tissue thickening. Histological exam reveals epidermic hiperplasia, collagen fibers and fibroblast proliferation and increased mucin deposition.
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